[A case of Pryce's type I pulmonary sequestration with hemoptysis and bruit]

A 20-year-old man was admitted to our hospital with the complaint of hemoptysis. A bruit was best heard at the lower portion of the left posterior chest. CT scan and MRI revealed clearly the existence of a large aberrant vessel from the descending thoracic aorta. Aorto- and pulmonary arteriography demonstrated that a large systemic artery from the descending thoracic aorta supplied the basilar segments of the left lower lobe, and to which there was no pulmonary artery supply. The pulmonary veins from these segments drained into the left atrium. The properative diagnosis was Pryce's type I pulmonary sequestration. A left lower lobectomy was performed. The aberrant vessel was 15 mm in diameter and was elastic walled. The systemic artery of the basilar segments revealed proliferation of media and obstructive changes. Some discussions were made about hemoptysis and bruit in 23 cases of Pryce's type I pulmonary sequestration in Japan.