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Acute cardiac tamponade secondary to congenital factor V deficiency
S C Schultz1, J Breall, R Hannan
1Division of Cardiovascular Surgery, Georgetown University School of Medicine, Washington, D.C., USA.
Cardiology
|January 1, 1997
Abstract:
Spontaneous cardiac tamponade secondary to a congenital coagulation defect has never been reported. We report a case of acute cardiac tamponade in a patient with a known factor V deficiency. This patient presented with classic signs of acute cardiac tamponade and an enlarged cardiac silhouette. After diagnostic two-dimensional echocardiography and treatment with fresh-frozen plasma, the patient underwent emergent pericardiocentesis followed by complete pericardiectomy.