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[Echographic aspects of Caroli disease]
G Ruffa1, G Lucigrai, M Bartocci
1II Clinica Pediatrica G Gaslini, Instituto Giannina Gaslini, Università degli Studi, Genova.
Minerva Pediatrica
|July 1, 1996
Summary
Caroli disease, a congenital bile duct condition, is accurately diagnosed using ultrasound, revealing ductal dilatation and bridging. Ursodeoxycholic acid effectively treats the associated chronic cholestasis.
Area of Science:
- Hepatology
- Radiology
- Medical Genetics
Background:
- Caroli disease is a rare congenital condition characterized by non-obstructive dilatation of the intrahepatic bile ducts.
- Chronic cholestasis is a common complication, necessitating effective management strategies.