Focal abnormalities in mitochondrial distribution in muscle. Two atypical cases of so-called "central core disease"
Acta Neuropathologica
|July 15, 1977
Abstract:
Describing two new cases of so-called Central Core Disease, the authors revealed certain atypical features: The cores were formed in central as well as in peripheral position; they were observed in some apparently type II fibers; typical "structured" and "unstructured" cores coexisted with "reversed" core. Starting from this pictures a cycle of core formation was imaginated supposing to be initiated as the consequence of abnormal functional interrelationship between muscular and neural components in early myogenesis.
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