Partial anomalous pulmonary venous drainage associated with intact atrial septum and pulmonary valve stenosis

Partial anomalous pulmonary venous drainage (PAPVD) with an intact atrial septum is a very rare cardiovascular anomaly. Most PAPVD cases can be detected by echocardiographic scanning of the anomalous pulmonary venous connection. This paper describes an asymptomatic 6-year-old boy who was referred because of a heart murmur. An electrocardiogram and two-dimensional echocardiography revealed right heart volume overload. Mild pulmonary valve stenosis and an intact atrial septum were noted. In addition, color flow mapping demonstrated the right upper pulmonary vein connecting to the superior vena cava. This paper emphasizes that two-dimensional echocardiography in conjunction with color flow mapping is a valuable modality in the detection of anomalous pulmonary venous drainage.