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[Hypertension secondary to multiple malignant paragangliomas]
A Mazza1, F Della Rocca, P Mormino
1Dipartimento di Medicina Clinica e Sperimentale (Cattedra di Medicina Interna), Università di Padova.
Summary
This case study details severe hypertension caused by multiple malignant norepinephrine-secreting paragangliomas. Surgical removal and radiotherapy were necessary, with ongoing medication required to manage high norepinephrine levels.
Area of Science:
- Endocrinology
- Oncology
- Nephrology
Background:
- Neuroendocrine tumors account for 0.1-0.5% of hypertension cases.
- Extra-adrenal paragangliomas represent about 10% of these tumors.
- Only 20% of paragangliomas secrete catecholamines, mimicking pheochromocytoma.