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Adult hemolytic-uremic syndrome. Familial variant
Archives of Internal Medicine
|September 1, 1977
Summary
This study details a family with inherited hemolytic-uremic syndrome (HUS). Adult family members experienced renal failure, hypertension, and early death, suggesting an autosomal dominant inheritance pattern for adult-onset HUS.
Area of Science:
- Nephrology
- Genetics
- Hematology
Background:
- Hemolytic-uremic syndrome (HUS) is a serious condition.
- Adult-onset HUS with a clear inheritance pattern is rare.