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The sickle cell hemolytic transfusion reaction syndrome
L D Petz1, L Calhoun, I A Shulman
1Division of Transfusion Medicine, University of California, Los Angeles 90095-1713, USA.
Transfusion
|April 1, 1997
Summary
Severe hemolytic transfusion reactions (HTRs) in sickle cell anemia can worsen anemia. This occurs when erythropoiesis is suppressed, leading to a rapid drop in hematocrit, especially when donor red cells are hemolyzed.
Area of Science:
- Hematology
- Transfusion Medicine
Background:
- Sickle cell anemia patients are at risk for severe, life-threatening hemolytic transfusion reactions (HTRs).
- Post-transfusion anemia can be more severe than pre-transfusion anemia, suggesting increased autologous red cell destruction.