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Malignant fibrous histocytoma producing spinal cord compression
Journal of Neurology, Neurosurgery, and Psychiatry
|September 1, 1979
Summary
Malignant fibrous histiocytoma can present as a paraspinal tumor causing spinal cord compression. While surgery offers pain relief, recurrence and poor prognosis with neurological deficits are common.
Area of Science:
- Oncology
- Neurosurgery
- Pathology
Background:
- Malignant fibrous histiocytoma (MFH) is a rare soft tissue sarcoma.
- Primary paraspinal tumors are uncommon causes of spinal cord compression.
Observation:
- Three cases of MFH presenting as primary paraspinal tumors are described.
- These tumors led to extradural spinal cord compression.
Findings:
- Laminectomy provided considerable pain relief in these cases.
- Pain recurrence was observed with further tumor growth.
- Complete tumor resection was not feasible.
- Diagnosis of paraspinal MFH is challenging.
- Post-operative neurological deficits persisted despite surgery and radiotherapy.
Implications:
- MFH requires a multidisciplinary approach for management.
- Prognosis for patients with paraspinal MFH and spinal cord compression is guarded.
- Further research into effective treatment strategies for paraspinal MFH is warranted.