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Prolidase deficiency and systemic lupus erythematosus
M Shrinath1, J H Walter, M Haeney
1Royal Manchester Children's Hospital.
Archives of Disease in Childhood
|May 1, 1997
Summary
Children with prolidase deficiency, a metabolic disorder, can develop systemic lupus erythematosus (SLE). Prolidase deficiency may be a risk factor for SLE, warranting further investigation in affected children.
Area of Science:
- Immunology
- Metabolic Disorders
- Pediatrics
Background:
- Prolidase deficiency is an inborn error of proline metabolism.
- Systemic lupus erythematosus (SLE) is an autoimmune disease with diverse clinical manifestations.
- Both conditions involve immune system dysfunction and share overlapping clinical features.