Clear-cell sarcoma of tendons and aponeuroses. Report of two cases

Two cases of clear-cell sarcoma of tendons and aponeuroses are reported. The first patient was a 19-year-old man with a tumor in the medial collateral ligament of the knee. The tumor was enucleated, and after postoperative radiotherapy a wide local excision was done. The patient was symptomless 4 1/2 years after the operation. The other patient was a man aged 68 with a tumor between the medial malleolus and the Achilles tendon. He also received postoperative radiotherapy after enucleation. Three months later a metastasis was noticed in the ipsilateral para-iliac nodes. The patient died 16 months after the operation. The histology and clinical course of the two cases are analyzed. Some integrative remarks based on earlier reports of 33 cases and the present two cases are presented.