Peripapillary staphyloma

J L Gottlieb1, D M Prieto, J F Vander

  • 1Wills Eye Hospital Retina Service, Philadelphia, PA 19107, USA.

Insights

A rare case of peripapillary staphyloma was identified in a 5-month-old infant. This condition, though uncommon, can lead to significant vision loss in the affected eye.

Area of Science:

  • Ophthalmology
  • Pediatric Ophthalmology

Background:

  • Peripapillary staphyloma is a rare condition characterized by outward bulging of the optic nerve head and surrounding sclera.
  • Early diagnosis and management are crucial for potential visual outcomes.

Observation:

  • A 5-month-old infant presented with esotropia and a significant retinal and optic nerve abnormality in the left eye.
  • The patient had no systemic abnormalities, and the right eye was unaffected.

Findings:

  • Diagnostic evaluations, including ultrasonography and electroretinography, confirmed a peripapillary staphyloma measuring 9.77 mm in depth in the left eye.
  • The findings highlight a severe, isolated ocular anomaly.

Implications:

  • This case underscores that peripapillary staphyloma, despite its rarity, can cause profound visual impairment in otherwise healthy infants.
  • Ophthalmologists should consider this diagnosis in infants with strabismus and optic nerve abnormalities.
Abstract