[Retrovesical schwannosarcoma]

Contribution of one case of retrovesical schwannosarcoma in a 23-year-old female patient, with discussion of signs and symptoms, diagnosis and treatment. Retroperitoneal schwannosarcoma is an extremely uncommon tumour. Diagnosis is always histologic and immunohistochemical. This is an extraordinary aggressive tumour, with low response to chemo- and radiotherapy. Surgery is the only curative treatment, and presents a high index of recurrence. Prognosis is sombre. We support the most radical surgical approach possible as the only definite diagnostic possibility, since it provides the best survival indexes and in any case, improves symptomatology of tumours not completely resectable.