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Bentall operation for a child with Marfan syndrome: a case report
M Miura1, Y Shimazaki, T Watanabe
1Second Department of Surgery, Yamagata University, School of Medicine, Japan.
Journal of Cardiac Surgery
|March 1, 1997
Abstract:
Children with Marfan syndrome rarely undergo surgery for annuloaortic ectasia and aortic regurgitation in the first decade. A 7-year-old girl presented with congestive heart failure due to severe aortic regurgitation associated with annuloaortic ectasia (6 cm). She also had funnel chest. She underwent a Bentall operation and sternal turn-over with a satisfactory result. Since the aortic valve cusps had rolled edges, the aortic valve was not spared. Histology of the aortic valve cusps showed myxoid degeneration and fragmentation of elastic fibers.