[A case of ossifying fibromyxoid tumor]

Recently described entity: ossifying fibromyxoid tumour of soft parts is presented. Schwann cell nature of the proliferating cells was demonstrated by immunohistochemical means. This special kind of nerve sheath tumors is characterised by pathological differentiation of the cells, resulting bone and in some cases additional cartilage formation. As for biological behaviour: in spite of occasional histological evidences of malignancy, no distant metastases are to be expected. Local aggressivity and recurrences may occur, thus designation is preferable as semimalignant or according to more modern terms as low-grade malignant tumour.