[Primary teratoma of the orbit. Apropos of a case]

Primary teratomas rarely occur in the orbit leading to major exophthalmia in the neonate. We report a case in a female infant who presented globular right exophthalmia extending beyond the orbit caused by a teratoma of the orbit. There was right ophthalmoplegia. Computed tomography showed enlargement of the orbit without modification of the bony structure despite the tumor volume. Tumoral enucleation was performed via the transconjunctive route. Histology reported benign mature multi-tissue teratoma. The postoperative course was uneventful. The CT-scan at 6 months evidence the absence of recurrence, outcome which has been confirmed after a 5-years follow-up.