[Evaluation of total cavopulmonary shunt operation from late results]

Total cavopulmonary shunt was performed in 6 patients (pts) with single ventricle and common atrioventricular valve (CAVV) with left isomerism between 1978 and 1987. Four patients survived including 1 with CAVV-replacement and follow-up period ranged from 1.5 to 10 years. The first pt tolerated a pregnancy and re-replacement of CAVV. All 4 pts showed significant improvements in symptom. The arterial oxygen saturation was around 90% early postoperatively, but 2 pts developed pulmonary arteriovenous fistula with decreased arterial oxygen saturation. This operation can be indicated in left isomerism with low operative risk, and also may be applied in those with CAVV regurgitation although the risk becomes high. PAVF is a matter of concern in the late follow-up.