[An operative case of partial anomalous pulmonary venous connection with systemic lupus erythematosus]

The patient was 43 years old female who was administrated by shortness of breath. Preoperative data including immunological examinations identified as SLE. Cardia angiogram showed PAPVC of the right pulmonary veins returned to the right atrium without ASD. Pulmonary hypertention was found with cardiac catheterizations. Open lung biopsy identified pulmonary hypertention caused by shunt volume load, but not by SLE. Surgical correction was accomplished by creating ASD and constructing a baffle to direct the blood flow from the right pulmonary veins to the left atrium. Resulting from this procedure was made pulmonary arterial pressure decreased to normal range.