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Sarcoid myopathy: imaging findings

C D Levine1, J J Miller, G Stanislaus

  • 1Department of Radiology, University of Medicine and Dentistry of New Jersey, Newark 07666, USA.

Journal of Clinical Ultrasound : JCU
|November 14, 1997
PubMed
Summary

Sarcoidosis can affect muscles, presenting as nodular, atrophic, or acute myositic forms. This case highlights an unusual myopathic sarcoidosis involving abdominal muscles, emphasizing its consideration in focal muscle disease diagnosis.

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Area of Science:

  • * Rheumatology and Immunology
  • * Neuromuscular Disorders

Background:

  • * Sarcoidosis is a multisystem granulomatous disease with rare muscle involvement.
  • * Muscular sarcoidosis presents in various forms, including nodular, atrophic myopathic, and acute myositic patterns.

Observation:

  • * A unique case of myopathic sarcoidosis involving abdominal wall muscles is presented.
  • * This contrasts with typical presentations primarily affecting extremity muscles.

Findings:

  • * Bilateral hilar adenopathy on chest radiography and abdominal findings like hepatosplenomegaly and retroperitoneal adenopathy can aid diagnosis.
  • * Sonographically guided biopsy may be required for definitive diagnosis when clinical signs are atypical.

Implications:

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  • * Muscular sarcoidosis should be included in the differential diagnosis of focal muscle diseases.
  • * Early consideration is crucial, particularly in patients with a known sarcoidosis history.
  • * Diagnostic imaging and biopsy are key for confirming this uncommon presentation.