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Expression of polycystin in mouse metanephros and extra-metanephric tissues

M D Griffin1, D A O'Sullivan, V E Torres

  • 1Nephrology Research Unit, Mayo Clinic, Rochester, Minnesota, USA.

Kidney International
|November 14, 1997
PubMed

Insights

Researchers identified the mouse polycystic kidney disease 1 gene (PKD1) on chromosome 17. Polycystin protein is expressed in various embryonic mouse tissues, including the developing kidney, suggesting its crucial role in development.

Area of Science:

  • Developmental Biology
  • Genetics
  • Molecular Biology

Background:

  • The polycystic kidney disease 1 (PKD1) gene is implicated in human autosomal dominant polycystic kidney disease.
  • Understanding the homologous gene and protein expression in model organisms is crucial for disease research.

Purpose of the Study:

  • To characterize the mouse homologue of the human PKD1 gene.
  • To investigate the expression pattern of polycystin during mouse embryonic development.

Main Methods:

  • Reverse transcription-polymerase chain reaction (RT-PCR) to detect PKD1 mRNA.
  • Fluorescent in situ hybridization to determine gene locus.
  • Immunoprecipitation and immunoperoxidase/immunofluorescent staining to detect polycystin protein expression.

Main Results:

  • A single mouse PKD1 gene locus was mapped to chromosome 17.
  • Polycystin protein, with high molecular weight bands (>400 kDa), was detected.
  • Polycystin expression was observed as early as day 8 of gestation in various embryonic tissues, including the developing kidney, liver, muscle, and neural tissues.

Conclusions:

  • The mouse possesses a single PKD1 gene homologous to the human gene, located on chromosome 17.
  • Polycystin is widely expressed in diverse tissues during mouse embryonic development, particularly in the developing kidney.
  • These findings provide a foundation for studying PKD1 function and related diseases in mice.

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