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Complications experienced with central venous catheters in children with congenital bleeding disorders

P W Collins1, K S Khair, R Liesner

  • 1The Haemophilia Comprehensive Care Centre, Great Ormond Street Hospital for Children NHS Trust, London.

Insights

Central venous catheters (CVCs) enable home treatment for children with bleeding disorders. However, CVC use in these patients is associated with significant line-associated infections, particularly in those with inhibitors.

Area of Science:

  • Pediatric Hematology
  • Infectious Diseases
  • Medical Devices

Background:

  • Central venous catheters (CVCs) are crucial for managing children with coagulation disorders, facilitating home treatment, prophylactic blood product replacement, and immune tolerance induction.
  • Prior literature suggested a low incidence of infective complications associated with CVC use in this pediatric population.

Purpose of the Study:

  • To evaluate the incidence and characteristics of line-associated infections in children with bleeding disorders who utilize CVCs.
  • To compare infection rates between children with and without inhibitors to factor VIII.

Main Methods:

  • Retrospective review of 23 pediatric patients with bleeding disorders who had 32 CVCs inserted.
  • Median follow-up of 27 months (range 1-92 months).
  • Documentation and analysis of all line-associated infections, including bloodstream infections and port site infections, and CVC removal reasons.

Main Results:

  • A total of 25 line-associated infections were documented, with 23 cases of bacteremia (1 episode per 26 patient-months at risk).
  • Infections occurred in 48% of patients, with Gram-positive organisms being the most common pathogens.
  • Patients with inhibitors to factor VIII experienced significantly higher infection rates (1 episode per 8.3 months) compared to those without inhibitors (1 episode per 50 months) (P<0.03).

Conclusions:

  • Despite a higher-than-expected rate of CVC-associated infections, CVCs remain a favored option for families managing children with bleeding disorders.
  • Close collaboration between families and experienced Hemophilia Center staff is essential for optimizing CVC safety and patient outcomes.
  • The findings highlight the need for vigilant infection surveillance and management strategies in pediatric patients with bleeding disorders using CVCs, especially those with inhibitors.

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