Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Related Experiment Videos

Cystic fibrosis

M L Aitken

    Current Opinion in Pulmonary Medicine
    |November 1, 1995
    PubMed
    Summary
    This summary is machine-generated.

    Cystic fibrosis (CF) survival has dramatically increased due to advancements in understanding and treatment. New therapies and genetic insights offer hope for longer lifespans for individuals with CF.

    Related Experiment Videos

    Related Concept Videos

    You might also read

    Related Articles

    Articles linked to this work by shared authors, journal, and citation graph.

    Sort by
    Same author

    Changes in fecal microbiota with CFTR modulator therapy: A pilot study.

    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society·2021
    Same author

    Men's health in the modern era of cystic fibrosis.

    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society·2020
    Same author

    Rationale and design of a randomized trial of home electronic symptom and lung function monitoring to detect cystic fibrosis pulmonary exacerbations: the early intervention in cystic fibrosis exacerbation (eICE) trial.

    Contemporary clinical trials·2013
    Same author

    Patient-reported respiratory symptoms in cystic fibrosis.

    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society·2009
    Same author

    Association between Stenotrophomonas maltophilia and lung function in cystic fibrosis.

    Thorax·2004
    Same author

    Malignant nerve-sheath tumor with divergent and glandular differentiation in a dog: a case report.

    Veterinary pathology·2002
    Same journal

    Nonsteroid treatment options in (pulmonary) sarcoidosis. When to consider and why?

    Current opinion in pulmonary medicine·2026
    Same journal

    Multidisciplinary approach in cardiac sarcoidosis: to biopsy or not?

    Current opinion in pulmonary medicine·2026
    Same journal

    Low diffusion capacity in pulmonary hypertension.

    Current opinion in pulmonary medicine·2026
    Same journal

    Toward precision imaging in interstitial lung disease: advances in quantitative imaging and artificial intelligence.

    Current opinion in pulmonary medicine·2026
    Same journal

    Oxygen therapy in interstitial lung disease - navigating benefit and burden.

    Current opinion in pulmonary medicine·2026
    Same journal

    Preclinical and clinical advances in pulmonary hypertension associated with systemic sclerosis.

    Current opinion in pulmonary medicine·2026
    See all related articles

    Area of Science:

    • Pulmonology and Genetics
    • Clinical Medicine

    Background:

    • Cystic fibrosis (CF) is a genetic disorder recognized clinically for under 60 years.
    • Median survival has risen from months to 29 years, highlighting significant medical progress.

    Discussion:

    • Review covers CF's multi-organ impact, management strategies, and evolving research areas.
    • Explores the role of the cystic fibrosis transmembrane conductance regulator (CFTR) in lung disease.
    • Discusses genotype-phenotype correlations, prognostic factors, and emerging treatments.

    Key Insights:

    • Lung transplantation and gene therapy offer future therapeutic avenues.
    • Understanding CFTR function is crucial for developing targeted therapies.
    • Genetics plays a key role in CF's presentation and progression.

    Outlook:

    • Projected increase in life expectancy for individuals with CF, reaching into their 40s.
    • Continued rapid advancements in clinical and genetic understanding promise improved outcomes.