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'Angiographic moyamoya' its definition, classification, and therapy
Y Natori1, K Ikezaki, T Matsushima
1Department of Neurosurgery, Kyushu University Faculty of Medicine, Fukuoka, Japan.
Clinical Neurology and Neurosurgery
|December 31, 1997
Summary
This study clarifies terminology for Moyamoya disease variants. It recommends using "probable Moyamoya disease" for unilateral cases and avoiding vague terms like "syndrome" or "quasi" for clarity.
Area of Science:
- Neurology
- Radiology
- Medical Terminology
Background:
- Moyamoya disease terminology is inconsistent, causing confusion.
- Distinctions between probable, unilateral, and definite Moyamoya disease require clarification.
- Patients with similar angiographic features due to systemic disorders are often mislabeled.
Purpose of the Study:
- To review and clarify the usage of terms related to Moyamoya disease.
- To establish standardized terminology for Moyamoya disease and its variants.
- To address the confusion arising from terms like Moyamoya syndrome, quasi-Moyamoya disease, and akin-Moyamoya disease.
Main Methods:
- Literature review of previously reported cases.
- Analysis of diagnostic criteria for Moyamoya disease.
- Survey of how various terms have been applied in published studies.
Main Results:
- The term "Moyamoya syndrome" is inappropriate given diagnostic criteria based on angiography.
- "Probable Moyamoya disease" is recommended for unilateral cases without a known cause.
- Vague terms like "quasi," "akin," and "pseudo" should be avoided to prevent misinterpretation and acknowledge potential co-existing conditions.
Conclusions:
- Standardized terminology is crucial for accurate Moyamoya disease diagnosis and research.
- Clearer definitions will improve communication among clinicians and researchers.
- Future research should focus on the etiology of Moyamoya disease to further refine classification.