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Rett syndrome: analysis of deaths in the British survey
A M Kerr1, D D Armstrong, R J Prescott
1Department of Psychological Medicine, Gartnavel Royal Hospital, Glasgow, Scotland.
European Child & Adolescent Psychiatry
|January 1, 1997
Abstract:
The mortality rate in Rett syndrome is 1.2% per annum, 48% of deaths occurring in debilitated people, 13% from natural causes, 13% with prior severe seizures and 26% sudden and unexpected. Respiratory dysrhythmias were usually present. Neuropathology confirmed reductions in cortical dendrites and in one case immaturity of cardiac conducting tissues.