Peters' anomaly associated with protruding corneal pseudo staphyloma

G W Zaidman1, K Juechter

  • 1Westchester Medical Center, Our Lady of Mercy Hospital, New York Medical College, Department of Ophthalmology, Valhalla 10595, USA.

Cornea
|March 31, 1998
PubMed

Insights

This study describes a novel Peters

Area of Science:

  • Ophthalmology
  • Genetics
  • Pediatric Medicine

Background:

  • Peters' anomaly is a rare congenital corneal defect.
  • It is characterized by a central corneal opacity and iridocorneal adhesions.
  • This condition can lead to severe vision impairment.

Observation:

  • Four infants presented with a unique Peters' anomaly manifestation.
  • Affected eyes showed thickened, scarred corneas resembling congenital anterior staphyloma.
  • Ocular findings varied from normal to severe anomalies in the contralateral eye.

Findings:

  • Corneal transplants were performed on affected eyes.
  • Three out of four corneal grafts maintained clarity for over a year.
  • Vision was restored in three eyes; two developed glaucoma.
  • Histopathology confirmed Peters' anomaly in corneal buttons.

Implications:

  • This presentation expands the spectrum of Peters' anomaly.
  • Surgical intervention (corneal transplant) improved cosmetic appearance and vision.
  • Early diagnosis and management are crucial for visual outcomes in Peters' anomaly.
Abstract