Chylous reflux into the lower limb with septic shock successfully treated by resection of the retroperitoneal megalymphatics

A 15-year-old boy with primary chylous reflux into the left lower limb with septic shock was successfully treated by en bloc resection and ligation of the retroperitoneal megalymphatics. The episode of chyle discharge from the lower limb and/or genitalia and the presence of small vesicles of the skin may be an important sign in diagnosing chylous reflux. Surgical interruption of the chylous reflux and reduction of girth may be needed.