Internal jugular vein malformation with mature adipose deposits in the mediastinum

Anomalies of the internal jugular vein are uncommon and not frequently experienced. Either a fusiform or saccular dilatation of the veins has been termed phlebectasia by some investigators and venous aneurysm by others. In 1928 Harris was the first to describe this condition using the term "congenital venous cyst." Relatively few cases of head and neck venous aneurysms have since been reported. We herein report a case of congenital internal jugular vein malformation while discussing both the diagnosis and pathology.