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Melanotic neuroectodermal tumor of infancy
C Hoeffel1, J M Vignaud, A Clement
1Service de Radiologie, Hôpital Jeanne d'Arc, Toul, France.
Klinische Padiatrie
|June 18, 1998
Summary
A rare melanotic neuroectodermal tumor was found in a 6-month-old infant's maxilla. Surgical excision led to a benign outcome for this neural crest tumor.
Area of Science:
- Pediatric Oncology
- Oral and Maxillofacial Surgery
- Pathology
Background:
- Melanotic neuroectodermal tumor (MNT) is an uncommon, benign neoplasm of neural crest origin.
- It predominantly affects infants and young children, with a strong predilection for the maxilla.
Observation:
- A 6-month-old female presented with a swelling of the left superior maxillary bone.
- Radiographic and CT imaging revealed a radiolucent lesion and a solid mass in the left anterior maxilla.
- Surgical exploration identified a cystic dental tumor in an ectopic location.
Findings:
- Pathological diagnosis confirmed melanotic neuroectodermal tumor.
- Imaging characteristics included a hyperdense mass on CT and specific signal intensities on MRI (hypointense on T1, iso-intense on T2).
- The tumor, though ectopic, was successfully treated by surgical excision.
Implications:
- Early diagnosis and surgical management are crucial for favorable outcomes in pediatric MNT.
- Understanding the typical and atypical presentations of MNT aids in accurate diagnosis and treatment planning.
- This case highlights the importance of considering MNT in the differential diagnosis of pediatric maxillary masses.