[A case of asplenia in a sickle cell homozygote SS patient]

One case of total splenic atrophy is reported in a patient with SS homozygous sickle-cell disease presenting no related malformation, thus recalling the IVEMARK syndrome. An abdominal echography and computed tomography are indispensable in order to confirm the absence of the anatomic spleen; this makes for a better follow-up of sickle-cell disease.