Primary localized amyloidosis of the ureter

Localized amyloidosis of the ureter is a relatively rare condition. We report a case of primary localized ureteral amyloidosis. A 66-year-old man was referred to our hospital complaining of right flank pain and gross hematuria. From the right hydronephrosis and irregular margin of the right lower ureter seen on the anterograde pyelography, we could not rule out a right ureteral malignancy. Total nephroureterectomy was performed and histologic examination showed ureteral amyloidosis. Amyloid was classified immunohistochemically as Alambda type. After all examinations for secondary or systemic amyloidosis were negative, primary localized amyloidosis of the ureter was confirmed.