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Suture supported P C IOL in a homocystinuric child
S S Bhatti1, A P Agashe, R P Jehangir
1Department of Ophthalmology, KEM Hospital, Parel, Mumbai 400012.
Insights
Homocystinuria in a child caused secondary glaucoma due to lens dislocation. Surgical lens removal and IOL implantation were successful, with complications managed effectively.
Area of Science:
- Ophthalmology
- Genetics
- Neurology
Background:
- Homocystinuria is a rare genetic metabolic disorder.
- Lens subluxation can lead to secondary glaucoma.
- Cerebral venous thrombosis is a serious neurological complication.
Observation:
- A child with homocystinuria presented with secondary pupillary block glaucoma.
- The glaucoma was caused by an anteriorly subluxated lens.
- Cerebral venous thrombosis occurred postoperatively following general anesthesia.
Findings:
- Successful surgical removal of the subluxated lens.
- Implantation of a suture-supported posterior chamber intraocular lens (IOL).
- Management of cerebral venous thrombosis with high-dose pyridoxine, special diet, and medication.
Implications:
- Highlights the ocular manifestations of homocystinuria.
- Demonstrates effective surgical management of lens-induced glaucoma.
- Emphasizes the importance of managing postoperative complications in pediatric patients.
Abstract:
A homocystinuric child presented with a secondary pupillary block glaucoma due to anteriorly subluxated lens. After removal of the subluxated lens, a suture supported posterior chamber IOL was implanted. Postoperative complication of cerebral venous thrombosis following general anaesthesia was managed with high doses of pyridoxine special diet and drugs.
