[Which perioperative therapeutic strategies in constitutional hemostasis disorders?]

Type A and B haemophilias and von Willebrand's disease are the most common haemostasis disorders. Haemorrhage risks during both surgery and the time period surrounding surgery are often associated with these diseases. Consequently, normalization of the plasma level of the lacking protein and adapted therapeutic management will be the main objectives. Before undertaking any surgical procedure, the interview with the anaesthesiologist will allow detection of the disease. The type and the severity of the deficit at the origin of perioperative haemorrhage risks may be determined in collaboration with appropriate treatment centers. Therapeutic procedures (under the form of a protocol) will thus be defined. This multidisciplinary approach will make any surgical procedure feasible, whatever the type of haemostasis disorder.