Two cases of primary pulmonary hypertension diagnosed during pregnancy

Primary pulmonary hypertension (PPH) is a rare clinical entity with a high mortality in pregnancy, delivery and postpartum. This paper describes two clinical cases of PPH diagnosed in pregnancy with different severity and outcomes; Case 1 was diagnosed as PPH at 34 weeks of gestation with pulmonary arterial pressure of 60 mmHg and delivered successfully by cesarean section with uneventful postoperative course. Case 2 was diagnosed as PPH at 26 weeks of gestation with pulmonary arterial pressure of 120 mmHg and delivered by cesarean section but died on the 7th day after the operation because of serious and progressive pulmonary hypertension. Patients with primary pulmonary hypertension should avoid pregnancy because of the high mortality, although some cases including ours have been reported with positive outcome.