Scleromyxedema (papular mucinosis): a surgical perspective

Scleromyxedema (papular mucinosis) is a rare systemic disorder with a poor prognosis that produces severe aesthetic and functional disability. A patient is presented for whom the hitherto undescribed use of aggressive surgical intervention for palliation is applied. Methods are described, including a discussion of the trial-and-error evolution of the treatment. Results are shown that suggest that there is a place for surgical intervention in the treatment of the cutaneous changes produced by this disease.