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Chronotropic competence of the sinus node in congenital complete heart block

A Menon1, E D Silverman, R M Gow

  • 1Department of Pediatrics, The Hospital for Sick Children, and the University of Toronto, Ontario, Canada.

Insights

Children exposed to anti-Ro antibodies can develop sinus node disease. Congenital complete heart block may also present with sinus node dysfunction, specifically chronotropic incompetence during exercise.

Area of Science:

  • Pediatric Cardiology
  • Electrophysiology
  • Neonatal Immunology

Background:

  • Maternal autoantibodies, such as anti-Ro antibodies, can cross the placenta.
  • Neonatal heart block is a known complication of transplacental antibody exposure.
  • Sinus node dysfunction can manifest in various pediatric cardiac conditions.

Purpose of the Study:

  • To investigate the prevalence and characteristics of sinus node disease in children with transplacental anti-Ro antibody exposure.
  • To evaluate sinus node function during exercise in children diagnosed with congenital complete heart block.

Main Methods:

  • Resting electrocardiogram (ECG) analysis in 2 children with transplacental anti-Ro antibody exposure and 1:1 atrioventricular conduction.
  • Treadmill exercise testing in 28 patients with congenital complete heart block.

Main Results:

  • Sinus node disease was identified in 2 children exposed to anti-Ro antibodies.
  • Chronotropic incompetence of the sinus node was observed in 3 out of 28 patients (10.7%) with congenital complete heart block during exercise testing.

Conclusions:

  • Transplacental anti-Ro antibody exposure is associated with sinus node disease in neonates.
  • Sinus node dysfunction, including chronotropic incompetence, is a potential complication in pediatric patients with congenital complete heart block.

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