[A case of congenital uveal ectropion with glaucoma]

A case of 21-year-old man with a rare congenital syndrome of uveal ectropion with glaucoma is described. The visual acuity was 1.0 with correction cyl. -1.0 axis 100 degrees. The highest intraocular pressure was 55 mm Hg. The optic nerve was damaged with glaucomatous cupping (cup/disc ratio 0.8). The visual field presented adequate few insular scotomas. The glaucoma filtering surgery was performed: goniotrepanatio by Fronimopoulos. After the surgery in one year observation intraocular pressure was about 15 mm Hg. The perimetry showed no increase in optic disc damage. We wanted to present this case because of its rare occurrence and good results of the surgery.