Related Experiment Videos
[Localized diffuse pulmonary AL-amyloidosis]
J Abdulla1, N Maltboek, H Birgens
1Amtssygehuset i Gentofte, lungemedicinsk afdeling Y.
Ugeskrift for Laeger
|January 16, 1999
Abstract:
A 56 year-old woman was admitted due to exertional dyspnoea. Her chest x-ray and CT scanning showed widespread diffuse infiltrative changes in both lungs, associated with a pronounced decrease in diffusion capacity. Transbronchial biopsies showed primary (AL) amyloidosis. Systemic AL-amyloidosis was excluded and diagnosis of localised diffuse parenchymal pulmonary amyloidosis was established. Treatment with prednisolone and melphalan for one year has stabilised the condition. Lung transplantation will be considered in case of deterioration.