Glomerulocystic kidney. Report of a case

We describe a rare type of congenital renal cystic disease involving the Bowman capsule and adjacent abnormal tubules. The patient had a moderate degree of proteinuria, but otherwise normal renal function. Two subcapsular hepatic cysts manifested the only other visceral involvement. This case is morphologically similar to one previously reported. A purely descriptive morphologic term is suggested for this distinctive lesion, viz, glomerulocystic kidney.