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Echocardiographic Evaluation of Atrial Communications before Transcatheter Closure
Published on: February 8, 2022
Evaluation and management of pulmonary atresia with intact ventricular septum
1Department of Cardiovascular Surgery, Children's Hospital, Boston, MA 02115, USA.
Insights
Pulmonary atresia with intact ventricular septum (PA/IVS) management is evolving. Early diagnosis and interventions can improve outcomes for this complex congenital heart defect.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Pulmonary atresia with intact ventricular septum (PA/IVS) presents a spectrum of right ventricle hypoplasia.
- Treatment strategies range from univentricular to biventricular and hybrid repairs.
- Historically associated with poor outcomes, PA/IVS is seeing improved prognoses.
Purpose of the Study:
- To highlight the shift towards optimism in PA/IVS management.
- To emphasize the role of early diagnosis and intervention.
- To showcase innovative approaches in treating PA/IVS.
Main Methods:
- Review of current understanding and treatment paradigms for PA/IVS.
- Focus on advancements in diagnostic and interventional techniques.
- Exploration of novel surgical and catheter-based strategies.
Main Results:
- Refined early diagnosis facilitates timely intervention.
- Interventions aimed at promoting right ventricle flow and growth are crucial.
- Innovative techniques, including fetal surgery, are emerging.
Conclusions:
- Optimistic outcomes for PA/IVS are increasingly achievable.
- Early and targeted interventions are key to improving right ventricle function.
- Continued innovation in fetal, surgical, and catheter-based approaches is vital for PA/IVS treatment.
Abstract:
Pulmonary atresia with intact ventricular septum (PA/IVS) is a spectrum of diseases with varying severity of right ventricle hypoplasia and potential for biventricular, univentricular, or hybrid repairs. Pessimistic outcome measures for PA/IVS may give way to optimism with the refinement of early diagnosis and early intervention to encourage right ventricle flow and optimize growth. To this end, PA/IVS has become a focus of innovative interventions (e.g., fetal surgery) and new catheter-based and surgical techniques.
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