Ebstein's malformation. Surgical experience at the Mayo Clinic

Area of Science:

• Cardiology
• Cardiac Surgery
• Congenital Heart Disease

Background:

• Ebstein's malformation is a rare congenital heart defect.
• Surgical intervention is often necessary for symptomatic patients.

Purpose of the Study:

• To evaluate surgical outcomes for Ebstein's malformation.
• To compare different surgical techniques for Ebstein's malformation repair.

Main Methods:

• Retrospective review of 13 patients undergoing surgical repair for Ebstein's malformation.
• Analysis of surgical techniques including tricuspid annuloplasty, ventricular plication, and prosthetic valve replacement.

Main Results:

• Tricuspid annuloplasty with plication of the atrialized right ventricle had a 100% survival rate.
• Prosthetic valve replacement had a 20% survival rate.
• Functional classification improved in 80% of operative survivors.

Conclusions:

• Repair of the atrialized right ventricle is crucial for improved outcomes in Ebstein's malformation.
• Combined ventricular plication and tricuspid annuloplasty demonstrate superior early and late results compared to valve replacement.