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Journal of Inherited Metabolic Disease|January 1, 1996
ALDP expression in fibroblasts of patients with X-linked adrenoleukodystrophyS Kemp, P A Mooyer, P A Bolhuis, et al.Molecular Microbiology|November 1, 1996
Bacillus subtilis can modulate its capacity and specificity for protein secretion through temporally controlled expression of the sipS gene for signal peptidase IA Bolhuis, A Sorokin, V Azevedo, et al.Journal of Neurology|September 1, 1988
Prospect for enzyme therapy in glycogenosis II variants: a study on cultured muscle cellsA T van der Ploeg, P A Bolhuis, R A Wolterman, et al.Biochemical and Biophysical Research Communications|August 16, 1990
Rapid shift in genotype of human mitochondrial DNA in a family with Leber's hereditary optic neuropathyP A Bolhuis, E M Bleeker-Wagemakers, N J Ponne, et al.Journal of the Neurological Sciences|July 1, 1987
Breakdown of lysosomal glycogen in cultured fibroblasts from glycogenosis type II patients after uptake of acid alpha-glucosidaseA T van der Ploeg, M Kroos, J M van Dongen, et al.Biochimica Et Biophysica Acta|September 13, 1993
Regulation of the expression of mitochondrial proteins: relationship between mtDNA copy number and cytochrome-c oxidase activity in human cells and tissuesC Van den Bogert, H De Vries, M Holtrop, et al.Neuromuscular Disorders : NMD|July 23, 1998
Genetic heterogeneity in Miyoshi-type distal muscular dystrophyW H Linssen, M de Visser, N C Notermans, et al.The Journal of Biological Chemistry|August 24, 1999
Signal peptide peptidase- and ClpP-like proteins of Bacillus subtilis required for efficient translocation and processing of secretory proteinsA Bolhuis, A Matzen, H L Hyyryläinen, et al.Experimental Cell Research|November 1, 1984
Uptake and stability of human and bovine acid alpha-glucosidase in cultured fibroblasts and skeletal muscle cells from glycogenosis type II patientsA J Reuser, M A Kroos, N J Ponne, et al.European Journal of Cell Biology|August 1, 1993
Mitochondria in cultured human muscle cells depleted of mitochondrial DNAN H Herzberg, E Middelkoop, M Adorf, et al.Pageof 14