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Frontiers in Pharmacology|June 16, 2023
Effects of lumacaftor-ivacaftor therapy on cystic fibrosis transmembrane conductance regulator function in F508del homozygous patients with cystic fibrosis aged 2-11 yearsJulian Berges, Simon Y Graeber, Susanne Hämmerling, et al.Macromolecular Rapid Communications|August 21, 2021
Polyglycerol-Based Mucus-Inspired HydrogelsAntara Sharma, Boonya Thongrom, Sumati Bhatia, et al.European Journal of Pediatrics|January 26, 2012
Homozygous CFTR mutation M348K in a boy with respiratory symptoms and failure to thrive. Disease-causing mutation or benign alteration?Julia Hentschel, Gabriele Riesener, Heike Nelle, et al.Der Radiologe|June 8, 2019
Ten years of chest MRI for patients with cystic fibrosis : Translation from the bench to clinical routinePatricia Leutz-Schmidt, Monika Eichinger, Mirjam Stahl, et al.Respirology (Carlton, Vic.)|February 25, 2025
Functional Lung Imaging Identifies Peripheral Ventilation Changes in ꞵ-ENaC MiceNicole Reyne, Ronan Smith, Patricia Cmielewski, et al.Frontiers in Physiology|August 22, 2022
An optimized protocol for assessment of sputum macrorheology in health and muco-obstructive lung diseaseMirjam Völler, Annalisa Addante, Hanna Rulff, et al.Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society|June 11, 2011
The ENaC-overexpressing mouse as a model of cystic fibrosis lung diseaseZhe Zhou, Julia Duerr, Bjarki Johannesson, et al.Journal of Applied Physiology (Bethesda, Md. : 1985)|June 14, 2014
Lung arginase expression and activity is increased in cystic fibrosis mouse modelsThomas Jaecklin, Julia Duerr, Hailu Huang, et al.Frontiers in Medicine|June 21, 2024
Contrast agent-free functional magnetic resonance imaging with matrix pencil decomposition to quantify abnormalities in lung perfusion and ventilation in patients with cystic fibrosisFelix Doellinger, Grzegorz Bauman, Jobst Roehmel, et al.Immunopharmacology and Immunotoxicology|May 1, 1994
Acrylamide induced immunosuppression in rats and its modulation by 6-MFA, an interferon inducerS I Zaidi, S Raisuddin, K P Singh, et al.Pageof 38