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Orphanet Journal of Rare Diseases
|
July 25, 2020
Clinical and molecular basis of hepatocerebral mitochondrial DNA depletion syndrome in Japan: evaluation of outcomes after liver transplantation
Masaru Shimura, Naomi Kuranobu, Minako Ogawa-Tominaga, et al.
Journal of Clinical Immunology
|
September 28, 2023
Antibody Deficiency in Patients with Biallelic KARS1 Mutations
Francesco Saettini, Fabiola Guerra, Grazia Fazio, et al.
Biochemical and Biophysical Research Communications
|
March 8, 2011
A novel mutation of ALK2, L196P, found in the most benign case of fibrodysplasia ossificans progressiva activates BMP-specific intracellular signaling equivalent to a typical mutation, R206H
Satoshi Ohte, Masashi Shin, Hiroki Sasanuma, et al.
Journal of Human Genetics
|
August 19, 2011
HRAS mutants identified in Costello syndrome patients can induce cellular senescence: possible implications for the pathogenesis of Costello syndrome
Tetsuya Niihori, Yoko Aoki, Nobuhiko Okamoto, et al.
International Journal of Cardiology
|
July 23, 2021
Long-term prognosis and genetic background of cardiomyopathy in 223 pediatric mitochondrial disease patients
Atsuko Imai-Okazaki, Ayako Matsunaga, Yukiko Yatsuka, et al.
Pediatric Research
|
April 24, 2025
Cardiac dysfunction due to mitochondrial impairment assessed by human iPS cells caused by DNM1L mutations
Madori T Osawa, Yasunori Fujita, Kazuki Kagami, et al.
American Journal of Human Genetics
|
November 3, 2015
Intra-mitochondrial Methylation Deficiency Due to Mutations in SLC25A26
Yoshihito Kishita, Aleksandra Pajak, Nikhita Ajit Bolar, et al.
Biochemistry and Biophysics Reports
|
April 13, 2026
Quantification of glycosaminoglycans in dried blood spots, and evaluation of its usefulness as a secondary newborn screening test for mucopolysaccharidoses
Wataru Oboshi, Asami Hirakiyama, Masahiro Miura, et al.
Molecular Genetics and Metabolism
|
August 13, 2017
Newborn screening for carnitine palmitoyltransferase II deficiency using (C16+C18:1)/C2: Evaluation of additional indices for adequate sensitivity and lower false-positivity
Go Tajima, Keiichi Hara, Miyuki Tsumura, et al.
Brain : a Journal of Neurology
|
May 3, 2018
Mutations in COA7 cause spinocerebellar ataxia with axonal neuropathy
Yujiro Higuchi, Ryuta Okunushi, Taichi Hara, et al.
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of 15
Search research articles
Search
Showing results (121-130 of 144) with videos related to
Sort By:
Page
of 15
Orphanet Journal of Rare Diseases
|
July 25, 2020
Clinical and molecular basis of hepatocerebral mitochondrial DNA depletion syndrome in Japan: evaluation of outcomes after liver transplantation
Masaru Shimura, Naomi Kuranobu, Minako Ogawa-Tominaga, et al.
Journal of Clinical Immunology
|
September 28, 2023
Antibody Deficiency in Patients with Biallelic KARS1 Mutations
Francesco Saettini, Fabiola Guerra, Grazia Fazio, et al.
Biochemical and Biophysical Research Communications
|
March 8, 2011
A novel mutation of ALK2, L196P, found in the most benign case of fibrodysplasia ossificans progressiva activates BMP-specific intracellular signaling equivalent to a typical mutation, R206H
Satoshi Ohte, Masashi Shin, Hiroki Sasanuma, et al.
Journal of Human Genetics
|
August 19, 2011
HRAS mutants identified in Costello syndrome patients can induce cellular senescence: possible implications for the pathogenesis of Costello syndrome
Tetsuya Niihori, Yoko Aoki, Nobuhiko Okamoto, et al.
International Journal of Cardiology
|
July 23, 2021
Long-term prognosis and genetic background of cardiomyopathy in 223 pediatric mitochondrial disease patients
Atsuko Imai-Okazaki, Ayako Matsunaga, Yukiko Yatsuka, et al.
Pediatric Research
|
April 24, 2025
Cardiac dysfunction due to mitochondrial impairment assessed by human iPS cells caused by DNM1L mutations
Madori T Osawa, Yasunori Fujita, Kazuki Kagami, et al.
American Journal of Human Genetics
|
November 3, 2015
Intra-mitochondrial Methylation Deficiency Due to Mutations in SLC25A26
Yoshihito Kishita, Aleksandra Pajak, Nikhita Ajit Bolar, et al.
Biochemistry and Biophysics Reports
|
April 13, 2026
Quantification of glycosaminoglycans in dried blood spots, and evaluation of its usefulness as a secondary newborn screening test for mucopolysaccharidoses
Wataru Oboshi, Asami Hirakiyama, Masahiro Miura, et al.
Molecular Genetics and Metabolism
|
August 13, 2017
Newborn screening for carnitine palmitoyltransferase II deficiency using (C16+C18:1)/C2: Evaluation of additional indices for adequate sensitivity and lower false-positivity
Go Tajima, Keiichi Hara, Miyuki Tsumura, et al.
Brain : a Journal of Neurology
|
May 3, 2018
Mutations in COA7 cause spinocerebellar ataxia with axonal neuropathy
Yujiro Higuchi, Ryuta Okunushi, Taichi Hara, et al.
Page
of 15