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Nucleic Acids Research|October 24, 2013
Functional characterization of the common c.-32-13T>G mutation of GAA gene: identification of potential therapeutic agentsAndrea Dardis, Irene Zanin, Stefania Zampieri, et al.
Orphanet Journal of Rare Diseases|February 26, 2013
A human neuronal model of Niemann Pick C disease developed from stem cells isolated from patient's skinNatascha Bergamin, Andrea Dardis, Antonio Beltrami, et al.
Molecular Genetics and Metabolism|August 27, 2013
Efficacy of miglustat in Niemann-Pick C disease: a single centre experienceVirginia Maria Ginocchio, Adele D'Amico, Enrico Bertini, et al.
Human Molecular Genetics|April 6, 2017
Shortened primary cilium length and dysregulated Sonic hedgehog signaling in Niemann-Pick C1 diseaseSonia Canterini, Jessica Dragotto, Andrea Dardis, et al.
International Journal of Molecular Sciences|June 27, 2024
Deficiency of Glucocerebrosidase Activity beyond Gaucher Disease: PSAP and LIMP-2 DysfunctionsEleonora Pavan, Paolo Peruzzo, Silvia Cattarossi, et al.
Human Mutation|October 27, 2015
SMPD1 Mutation Update: Database and Comprehensive Analysis of Published and Novel VariantsStefania Zampieri, Mirella Filocamo, Annalisa Pianta, et al.
Orphanet Journal of Rare Diseases|September 2, 2017
Chronic pain in Gaucher disease: skeletal or neuropathic origin?Grazia Devigili, Michele De Filippo, Giovanni Ciana, et al.
Journal of Neurology|February 27, 2014
Central cholinergic dysfunction in the adult form of Niemann Pick disease type C: a further link with Alzheimer's disease?Fiore Manganelli, Raffaele Dubbioso, Rosa Iodice, et al.
Neurogenetics|September 2, 2008
Molecular and functional analysis of the HEXB gene in Italian patients affected with Sandhoff disease: identification of six novel allelesStefania Zampieri, Mirella Filocamo, Emanuele Buratti, et al.
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