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Annamaria Fra

Showing results (11-20 of 20) with videos related to

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The FEBS Journal|January 8, 2025
Identification of an exosite at the neutrophil elastase/alpha-1-antitrypsin interfaceRoberto Gangemi, Mattia Bignotti, Andrea Denardo, et al.
International Journal of Molecular Sciences|June 2, 2021
The Importance of N186 in the Alpha-1-Antitrypsin Shutter Region Is Revealed by the Novel Bologna Deficiency VariantRiccardo Ronzoni, Ilaria Ferrarotti, Emanuela D'Acunto, et al.
JCI Insight|July 8, 2025
Susceptibility of alpha-1 antitrypsin deficiency variants to polymer-blocking therapyRiccardo Ronzoni, Ibrahim Aldobiyan, Elena Miranda, et al.
The European Respiratory Journal|February 6, 2016
Polymers of Z α1-antitrypsin are secreted in cell models of diseaseAnnamaria Fra, Francesca Cosmi, Adriana Ordoñez, et al.
Science Advances|May 7, 2025
High-resolution characterization of ex vivo AAT polymers by solution-state NMR spectroscopySarah M Lowen, Christopher A Waudby, Alistair M Jagger, et al.
The FEBS Journal|May 16, 2017
The pathological Trento variant of alpha-1-antitrypsin (E75V) shows nonclassical behaviour during polymerizationElena Miranda, Ilaria Ferrarotti, Romina Berardelli, et al.
Biomedicines|August 26, 2023
Human iPSC-Derived 3D Hepatic Organoids in a Miniaturized Dynamic Culture SystemSerena Calamaio, Marialaura Serzanti, Jennifer Boniotti, et al.
JCI Insight|July 24, 2020
Intrahepatic heteropolymerization of M and Z alpha-1-antitrypsinMattia Laffranchi, Emma Lk Elliston, Elena Miranda, et al.
Clinical Chemistry and Laboratory Medicine|February 26, 2024
Quantification of circulating alpha-1-antitrypsin polymers associated with different <i>SERPINA1</i> genotypesAlice M Balderacchi, Mattia Bignotti, Stefania Ottaviani, et al.
American Journal of Respiratory Cell and Molecular Biology|April 18, 2023
Comprehensive Clinical Diagnostic Pipelines Reveal New Variants in Alpha-1 Antitrypsin DeficiencyStefania Ottaviani, Giulia Bartoli, Tomás P Carroll, et al.
Pageof 2

Showing results (11-20 of 20) with videos related to

Sort By:
Pageof 2
You have reached the last page of results.This site can display upto 20 results.
The FEBS Journal|January 8, 2025
Identification of an exosite at the neutrophil elastase/alpha-1-antitrypsin interfaceRoberto Gangemi, Mattia Bignotti, Andrea Denardo, et al.
International Journal of Molecular Sciences|June 2, 2021
The Importance of N186 in the Alpha-1-Antitrypsin Shutter Region Is Revealed by the Novel Bologna Deficiency VariantRiccardo Ronzoni, Ilaria Ferrarotti, Emanuela D'Acunto, et al.
JCI Insight|July 8, 2025
Susceptibility of alpha-1 antitrypsin deficiency variants to polymer-blocking therapyRiccardo Ronzoni, Ibrahim Aldobiyan, Elena Miranda, et al.
The European Respiratory Journal|February 6, 2016
Polymers of Z α1-antitrypsin are secreted in cell models of diseaseAnnamaria Fra, Francesca Cosmi, Adriana Ordoñez, et al.
Science Advances|May 7, 2025
High-resolution characterization of ex vivo AAT polymers by solution-state NMR spectroscopySarah M Lowen, Christopher A Waudby, Alistair M Jagger, et al.
The FEBS Journal|May 16, 2017
The pathological Trento variant of alpha-1-antitrypsin (E75V) shows nonclassical behaviour during polymerizationElena Miranda, Ilaria Ferrarotti, Romina Berardelli, et al.
Biomedicines|August 26, 2023
Human iPSC-Derived 3D Hepatic Organoids in a Miniaturized Dynamic Culture SystemSerena Calamaio, Marialaura Serzanti, Jennifer Boniotti, et al.
JCI Insight|July 24, 2020
Intrahepatic heteropolymerization of M and Z alpha-1-antitrypsinMattia Laffranchi, Emma Lk Elliston, Elena Miranda, et al.
Clinical Chemistry and Laboratory Medicine|February 26, 2024
Quantification of circulating alpha-1-antitrypsin polymers associated with different <i>SERPINA1</i> genotypesAlice M Balderacchi, Mattia Bignotti, Stefania Ottaviani, et al.
American Journal of Respiratory Cell and Molecular Biology|April 18, 2023
Comprehensive Clinical Diagnostic Pipelines Reveal New Variants in Alpha-1 Antitrypsin DeficiencyStefania Ottaviani, Giulia Bartoli, Tomás P Carroll, et al.
Pageof 2