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C Jakobs

Showing results (161-170 of 417) with videos related to

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Clinical Neurophysiology : Official Journal of the International Federation of Clinical Neurophysiology|May 12, 2004
Photosensitive absence epilepsy with myoclonias and heterozygosity for succinic semialdehyde dehydrogenase (SSADH) deficiencyA Dervent, K M Gibson, P L Pearl, et al.
Journal of Inherited Metabolic Disease|November 5, 1997
A new peroxisomal beta-oxidation disorder in twin neonates: defective oxidation of both cerotic and pristanic acidsE Christensen, S A Pedersen, H Leth, et al.
Journal of Inherited Metabolic Disease|January 1, 1991
Liver transplantation in two children with tyrosinaemia type I: biochemical aspectsE Riudor, A Ribes, J Lloret, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|November 15, 1984
Stable isotope dilution analysis of orotic acid and uracil in amniotic fluidC Jakobs, L Sweetman, W L Nyhan, et al.
Journal of Inherited Metabolic Disease|November 20, 1998
The metabolism of phytanic acid and pristanic acid in man: a reviewN M Verhoeven, R J Wanders, B T Poll-The, et al.
The Journal of Cell Biology|October 26, 2005
Retinal ganglion cell degeneration is topological but not cell type specific in DBA/2J miceTatjana C Jakobs, Richard T Libby, Yixin Ben, et al.
Journal of Inherited Metabolic Disease|September 3, 1999
Spontaneous pregnancy in a patient with classical galactosaemiaS de Jongh, P Vreken, L IJst, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|November 30, 1990
Stable isotope dilution analysis of very long chain fatty acids in plasma, urine and amniotic fluid by electron capture negative ion mass fragmentographyF Stellaard, H J ten Brink, R M Kok, et al.
Journal of Inherited Metabolic Disease|January 1, 1993
Diagnosis of Zellweger syndrome by analysis of very long-chain fatty acids in stored blood spots collected at neonatal screeningC Jakobs, C M van den Heuvel, F Stellaard, et al.
Biochemical and Biophysical Research Communications|August 8, 1997
Resolution of the phytanic acid alpha-oxidation pathway: identification of pristanal as product of the decarboxylation of 2-hydroxyphytanoyl-CoAN M Verhoeven, D S Schor, H J ten Brink, et al.
Pageof 42

Showing results (161-170 of 417) with videos related to

Sort By:
Pageof 42
Clinical Neurophysiology : Official Journal of the International Federation of Clinical Neurophysiology|May 12, 2004
Photosensitive absence epilepsy with myoclonias and heterozygosity for succinic semialdehyde dehydrogenase (SSADH) deficiencyA Dervent, K M Gibson, P L Pearl, et al.
Journal of Inherited Metabolic Disease|November 5, 1997
A new peroxisomal beta-oxidation disorder in twin neonates: defective oxidation of both cerotic and pristanic acidsE Christensen, S A Pedersen, H Leth, et al.
Journal of Inherited Metabolic Disease|January 1, 1991
Liver transplantation in two children with tyrosinaemia type I: biochemical aspectsE Riudor, A Ribes, J Lloret, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|November 15, 1984
Stable isotope dilution analysis of orotic acid and uracil in amniotic fluidC Jakobs, L Sweetman, W L Nyhan, et al.
Journal of Inherited Metabolic Disease|November 20, 1998
The metabolism of phytanic acid and pristanic acid in man: a reviewN M Verhoeven, R J Wanders, B T Poll-The, et al.
The Journal of Cell Biology|October 26, 2005
Retinal ganglion cell degeneration is topological but not cell type specific in DBA/2J miceTatjana C Jakobs, Richard T Libby, Yixin Ben, et al.
Journal of Inherited Metabolic Disease|September 3, 1999
Spontaneous pregnancy in a patient with classical galactosaemiaS de Jongh, P Vreken, L IJst, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|November 30, 1990
Stable isotope dilution analysis of very long chain fatty acids in plasma, urine and amniotic fluid by electron capture negative ion mass fragmentographyF Stellaard, H J ten Brink, R M Kok, et al.
Journal of Inherited Metabolic Disease|January 1, 1993
Diagnosis of Zellweger syndrome by analysis of very long-chain fatty acids in stored blood spots collected at neonatal screeningC Jakobs, C M van den Heuvel, F Stellaard, et al.
Biochemical and Biophysical Research Communications|August 8, 1997
Resolution of the phytanic acid alpha-oxidation pathway: identification of pristanal as product of the decarboxylation of 2-hydroxyphytanoyl-CoAN M Verhoeven, D S Schor, H J ten Brink, et al.
Pageof 42