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C Jakobs

Showing results (171-180 of 417) with videos related to

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Journal of Chromatography. B, Analytical Technologies in the Biomedical and Life Sciences|October 18, 2002
Quantification of 3-hydroxyglutaric acid in urine, plasma, cerebrospinal fluid and amniotic fluid by stable-isotope dilution negative chemical ionization gas chromatography-mass spectrometryD S M Schor, N M Verhoeven, E A Struys, et al.
European Journal of Obstetrics, Gynecology, and Reproductive Biology|November 1, 1994
Amino acids, glucose and lactate concentrations in umbilical cord blood in relation to umbilical artery flow patternsV H Karsdorp, J M van Vugt, C Jakobs, et al.
FEBS Letters|July 14, 1998
Involvement of microsomal fatty aldehyde dehydrogenase in the alpha-oxidation of phytanic acidN M Verhoeven, C Jakobs, G Carney, et al.
Neuropediatrics|February 7, 1998
L-2-hydroxyglutaric aciduria: clinical heterogeneity versus biochemical homogeneity in a sibshipJ B de Klerk, J G Huijmans, H Stroink, et al.
European Journal of Pediatrics|November 1, 1988
Prenatal diagnosis of Zellweger syndrome by determination of trihydroxycoprostanic acid in amniotic fluidF Stellaard, S A Langelaar, R M Kok, et al.
Journal of Inherited Metabolic Disease|January 1, 1995
Phytanic acid oxidation in man: identification of a new enzyme catalysing the formation of 2-ketophytanic acid from 2-hydroxyphytanic acid and its deficiency in the Zellweger syndromeR J Wanders, C W van Roermund, D S Schor, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|September 15, 1983
Succinic semialdehyde dehydrogenase deficiency: an inborn error of gamma-aminobutyric acid metabolismK M Gibson, L Sweetman, W L Nyhan, et al.
Clinical Genetics|September 13, 2001
Molecular genetic analysis of the cystathionine beta-synthase gene in Portuguese homocystinuria patients: three novel mutationsR Castro, S G Heil, I Rivera, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|February 15, 1988
Stable isotope dilution analysis of succinylacetone using electron capture negative ion mass fragmentography: an accurate approach to the pre- and neonatal diagnosis of hereditary tyrosinemia type IC Jakobs, L Dorland, B Wikkerink, et al.
Journal of Inherited Metabolic Disease|January 26, 2006
Severe hypoglycaemia in isolated 3-methylcrotonyl-CoA carboxylase deficiency; a rare, severe clinical presentationH G M Oude Luttikhuis, G Touati, D Rabier, et al.
Pageof 42

Showing results (171-180 of 417) with videos related to

Sort By:
Pageof 42
Journal of Chromatography. B, Analytical Technologies in the Biomedical and Life Sciences|October 18, 2002
Quantification of 3-hydroxyglutaric acid in urine, plasma, cerebrospinal fluid and amniotic fluid by stable-isotope dilution negative chemical ionization gas chromatography-mass spectrometryD S M Schor, N M Verhoeven, E A Struys, et al.
European Journal of Obstetrics, Gynecology, and Reproductive Biology|November 1, 1994
Amino acids, glucose and lactate concentrations in umbilical cord blood in relation to umbilical artery flow patternsV H Karsdorp, J M van Vugt, C Jakobs, et al.
FEBS Letters|July 14, 1998
Involvement of microsomal fatty aldehyde dehydrogenase in the alpha-oxidation of phytanic acidN M Verhoeven, C Jakobs, G Carney, et al.
Neuropediatrics|February 7, 1998
L-2-hydroxyglutaric aciduria: clinical heterogeneity versus biochemical homogeneity in a sibshipJ B de Klerk, J G Huijmans, H Stroink, et al.
European Journal of Pediatrics|November 1, 1988
Prenatal diagnosis of Zellweger syndrome by determination of trihydroxycoprostanic acid in amniotic fluidF Stellaard, S A Langelaar, R M Kok, et al.
Journal of Inherited Metabolic Disease|January 1, 1995
Phytanic acid oxidation in man: identification of a new enzyme catalysing the formation of 2-ketophytanic acid from 2-hydroxyphytanic acid and its deficiency in the Zellweger syndromeR J Wanders, C W van Roermund, D S Schor, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|September 15, 1983
Succinic semialdehyde dehydrogenase deficiency: an inborn error of gamma-aminobutyric acid metabolismK M Gibson, L Sweetman, W L Nyhan, et al.
Clinical Genetics|September 13, 2001
Molecular genetic analysis of the cystathionine beta-synthase gene in Portuguese homocystinuria patients: three novel mutationsR Castro, S G Heil, I Rivera, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|February 15, 1988
Stable isotope dilution analysis of succinylacetone using electron capture negative ion mass fragmentography: an accurate approach to the pre- and neonatal diagnosis of hereditary tyrosinemia type IC Jakobs, L Dorland, B Wikkerink, et al.
Journal of Inherited Metabolic Disease|January 26, 2006
Severe hypoglycaemia in isolated 3-methylcrotonyl-CoA carboxylase deficiency; a rare, severe clinical presentationH G M Oude Luttikhuis, G Touati, D Rabier, et al.
Pageof 42