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C Jakobs

Showing results (241-250 of 417) with videos related to

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Journal of Inherited Metabolic Disease|January 1, 1993
Peroxisomal disorders: concentrations of metabolites in cerebrospinal fluid compared with plasmaH J ten Brink, C M van den Heuvel, B T Poll-The, et al.
QJM : Monthly Journal of the Association of Physicians|March 26, 2003
5,10-Methylenetetrahydrofolate reductase 677C-->T and 1298A-->C mutations are genetic determinants of elevated homocysteineR Castro, I Rivera, P Ravasco, et al.
Brain & Development|November 6, 2007
L-2-Hydroxyglutaric aciduria presenting with severe autistic featuresD I Zafeiriou, A Ververi, G S Salomons, et al.
Biochimica Et Biophysica Acta|February 16, 2007
Lipid abnormalities in succinate semialdehyde dehydrogenase (Aldh5a1-/-) deficient mouse brain provide additional evidence for myelin alterationsG Barcelo-Coblijn, E J Murphy, K Mills, et al.
Neuropediatrics|August 1, 1990
Acute hemiparesis as the presenting sign in a heterozygote for ornithine transcarbamylase deficiencyT J de Grauw, L M Smit, M Brockstedt, et al.
Journal of Inherited Metabolic Disease|January 1, 1996
L-2-Hydroxyglutaric aciduria: neuropathological correlations and first report of severe neurodegenerative disease and neonatal deathE Chen, W L Nyhan, C Jakobs, et al.
Journal of Inherited Metabolic Disease|January 1, 1996
Congenital nephrotic syndrome: a novel phenotype of type I carbohydrate-deficient glycoprotein syndromeM S van der Knaap, R A Wevers, L Monnens, et al.
Biomedical & Environmental Mass Spectrometry|February 1, 1990
Stable isotope dilution analysis of 4-hydroxybutyric acid: an accurate method for quantification in physiological fluids and the prenatal diagnosis of 4-hydroxybutyric aciduriaK M Gibson, S Aramaki, L Sweetman, et al.
Journal of Inherited Metabolic Disease|August 1, 1998
L-2-hydroxyglutaric aciduria and lactic acidosisP G Barth, R J Wanders, H R Scholte, et al.
Proceedings of the National Academy of Sciences of the United States of America|August 5, 1998
Hepatocyte injury in tyrosinemia type 1 is induced by fumarylacetoacetate and is inhibited by caspase inhibitorsS Kubo, M Sun, M Miyahara, et al.
Pageof 42

Showing results (241-250 of 417) with videos related to

Sort By:
Pageof 42
Journal of Inherited Metabolic Disease|January 1, 1993
Peroxisomal disorders: concentrations of metabolites in cerebrospinal fluid compared with plasmaH J ten Brink, C M van den Heuvel, B T Poll-The, et al.
QJM : Monthly Journal of the Association of Physicians|March 26, 2003
5,10-Methylenetetrahydrofolate reductase 677C-->T and 1298A-->C mutations are genetic determinants of elevated homocysteineR Castro, I Rivera, P Ravasco, et al.
Brain & Development|November 6, 2007
L-2-Hydroxyglutaric aciduria presenting with severe autistic featuresD I Zafeiriou, A Ververi, G S Salomons, et al.
Biochimica Et Biophysica Acta|February 16, 2007
Lipid abnormalities in succinate semialdehyde dehydrogenase (Aldh5a1-/-) deficient mouse brain provide additional evidence for myelin alterationsG Barcelo-Coblijn, E J Murphy, K Mills, et al.
Neuropediatrics|August 1, 1990
Acute hemiparesis as the presenting sign in a heterozygote for ornithine transcarbamylase deficiencyT J de Grauw, L M Smit, M Brockstedt, et al.
Journal of Inherited Metabolic Disease|January 1, 1996
L-2-Hydroxyglutaric aciduria: neuropathological correlations and first report of severe neurodegenerative disease and neonatal deathE Chen, W L Nyhan, C Jakobs, et al.
Journal of Inherited Metabolic Disease|January 1, 1996
Congenital nephrotic syndrome: a novel phenotype of type I carbohydrate-deficient glycoprotein syndromeM S van der Knaap, R A Wevers, L Monnens, et al.
Biomedical & Environmental Mass Spectrometry|February 1, 1990
Stable isotope dilution analysis of 4-hydroxybutyric acid: an accurate method for quantification in physiological fluids and the prenatal diagnosis of 4-hydroxybutyric aciduriaK M Gibson, S Aramaki, L Sweetman, et al.
Journal of Inherited Metabolic Disease|August 1, 1998
L-2-hydroxyglutaric aciduria and lactic acidosisP G Barth, R J Wanders, H R Scholte, et al.
Proceedings of the National Academy of Sciences of the United States of America|August 5, 1998
Hepatocyte injury in tyrosinemia type 1 is induced by fumarylacetoacetate and is inhibited by caspase inhibitorsS Kubo, M Sun, M Miyahara, et al.
Pageof 42