Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Filters

Claudia Compagnucci

Showing results (31-40 of 50) with videos related to

Pageof 5
Sort By:
Disease Models & Mechanisms|January 20, 2021
Altered cytoskeletal arrangement in induced pluripotent stem cells (iPSCs) and motor neurons from patients with riboflavin transporter deficiencyAlessia Niceforo, Chiara Marioli, Fiorella Colasuonno, et al.
Frontiers in Cell and Developmental Biology|January 21, 2025
Altered cytoskeleton dynamics in patient-derived iPSC-based model of PCDH19 clustering epilepsyRossella Borghi, Stefania Petrini, Valentina Apollonio, et al.
Stem Cells Translational Medicine|May 11, 2016
Rho Kinase Inhibition Is Essential During In Vitro Neurogenesis and Promotes Phenotypic Rescue of Human Induced Pluripotent Stem Cell-Derived Neurons With Oligophrenin-1 Loss of FunctionClaudia Compagnucci, Sabina Barresi, Stefania Petrini, et al.
Epilepsia|January 15, 2016
PCDH19-related epilepsy in two mosaic male patientsAlessandra Terracciano, Marina Trivisano, Raffaella Cusmai, et al.
Oxidative Medicine and Cellular Longevity|August 29, 2020
Mitochondrial and Peroxisomal Alterations Contribute to Energy Dysmetabolism in Riboflavin Transporter DeficiencyFiorella Colasuonno, Alessia Niceforo, Chiara Marioli, et al.
Plos One|February 2, 2013
Type-1 (CB1) cannabinoid receptor promotes neuronal differentiation and maturation of neural stem cellsClaudia Compagnucci, Sara Di Siena, Maria Blaire Bustamante, et al.
Cell Death Discovery|January 26, 2024
Caspase-dependent apoptosis in Riboflavin Transporter Deficiency iPSCs and derived motor neuronsChiara Marioli, Maurizio Muzzi, Fiorella Colasuonno, et al.
Human Molecular Genetics|August 13, 2016
Frataxin silencing alters microtubule stability in motor neurons: implications for Friedreich's ataxiaEmanuela Piermarini, Daniele Cartelli, Anna Pastore, et al.
Frontiers in Cellular Neuroscience|March 26, 2025
Riboflavin transporter deficiency: <i>AAV9-SLC52A2</i> gene therapy as a new therapeutic strategyCecilia Mei, Valentina Magliocca, Xin Chen, et al.
Frontiers in Cellular Neuroscience|August 8, 2024
Modeling riboflavin transporter deficiency type 2: from iPSC-derived motoneurons to iPSC-derived astrocytesValentina Magliocca, Angela Lanciotti, Elena Ambrosini, et al.
Pageof 5

Showing results (31-40 of 50) with videos related to

Sort By:
Pageof 5
Disease Models & Mechanisms|January 20, 2021
Altered cytoskeletal arrangement in induced pluripotent stem cells (iPSCs) and motor neurons from patients with riboflavin transporter deficiencyAlessia Niceforo, Chiara Marioli, Fiorella Colasuonno, et al.
Frontiers in Cell and Developmental Biology|January 21, 2025
Altered cytoskeleton dynamics in patient-derived iPSC-based model of PCDH19 clustering epilepsyRossella Borghi, Stefania Petrini, Valentina Apollonio, et al.
Stem Cells Translational Medicine|May 11, 2016
Rho Kinase Inhibition Is Essential During In Vitro Neurogenesis and Promotes Phenotypic Rescue of Human Induced Pluripotent Stem Cell-Derived Neurons With Oligophrenin-1 Loss of FunctionClaudia Compagnucci, Sabina Barresi, Stefania Petrini, et al.
Epilepsia|January 15, 2016
PCDH19-related epilepsy in two mosaic male patientsAlessandra Terracciano, Marina Trivisano, Raffaella Cusmai, et al.
Oxidative Medicine and Cellular Longevity|August 29, 2020
Mitochondrial and Peroxisomal Alterations Contribute to Energy Dysmetabolism in Riboflavin Transporter DeficiencyFiorella Colasuonno, Alessia Niceforo, Chiara Marioli, et al.
Plos One|February 2, 2013
Type-1 (CB1) cannabinoid receptor promotes neuronal differentiation and maturation of neural stem cellsClaudia Compagnucci, Sara Di Siena, Maria Blaire Bustamante, et al.
Cell Death Discovery|January 26, 2024
Caspase-dependent apoptosis in Riboflavin Transporter Deficiency iPSCs and derived motor neuronsChiara Marioli, Maurizio Muzzi, Fiorella Colasuonno, et al.
Human Molecular Genetics|August 13, 2016
Frataxin silencing alters microtubule stability in motor neurons: implications for Friedreich's ataxiaEmanuela Piermarini, Daniele Cartelli, Anna Pastore, et al.
Frontiers in Cellular Neuroscience|March 26, 2025
Riboflavin transporter deficiency: <i>AAV9-SLC52A2</i> gene therapy as a new therapeutic strategyCecilia Mei, Valentina Magliocca, Xin Chen, et al.
Frontiers in Cellular Neuroscience|August 8, 2024
Modeling riboflavin transporter deficiency type 2: from iPSC-derived motoneurons to iPSC-derived astrocytesValentina Magliocca, Angela Lanciotti, Elena Ambrosini, et al.
Pageof 5