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Déborah Mathis

Showing results (1-10 of 26) with videos related to

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Molecular Genetics and Metabolism Reports|December 13, 2021
Diagnosis of atypical myopathy based on organic acid and acylcarnitine profiles and evolution of biomarkers in surviving horsesDéborah Mathis, Jörn Oliver Sass, Claudia Graubner, et al.
Journal of Inherited Metabolic Disease|February 16, 2019
New insights into human lysine degradation pathways with relevance to pyridoxine-dependent epilepsy due to antiquitin deficiencyLisa M Crowther, Déborah Mathis, Martin Poms, et al.
Journal of Inherited Metabolic Disease|April 23, 2020
LC-MS/MS method for the differential diagnosis of treatable early onset inherited metabolic epilepsiesDéborah Mathis, Karin Beese, Carmen Rüegg, et al.
Journal of Inherited Metabolic Disease|September 5, 2024
Intra- and extracellular real-time analysis of perfused fibroblasts using an NMR bioreactor: A pilot studyChristian Urzì, Christoph Meyer, Déborah Mathis, et al.
Diabetologia|July 8, 2025
Dapagliflozin's impact on hormonal regulation and ketogenesis in type 1 diabetes: a randomised controlled crossover trialAndreas Gübeli, Nicole Steiner, Andreas Limacher, et al.
Genes|October 27, 2022
<i>ACADM</i> Frameshift Variant in Cavalier King Charles Spaniels with Medium-Chain Acyl-CoA Dehydrogenase DeficiencyMatthias Christen, Jos Bongers, Déborah Mathis, et al.
JIMD Reports|March 17, 2021
Decrease of disease-related metabolites upon fasting in a hemizygous knock-in mouse model (<i>Mut</i>-ko/ki) of methylmalonic aciduriaMarie Lucienne, Déborah Mathis, Nathan Perkins, et al.
Journal of the American Chemical Society|May 30, 2008
Artificial metalloenzyme for enantioselective sulfoxidation based on vanadyl-loaded streptavidinAnca Pordea, Marc Creus, Jaroslaw Panek, et al.
Journal of Inherited Metabolic Disease|May 13, 2022
The role of ERNDIM diagnostic proficiency schemes in improving the quality of diagnostic testing for inherited metabolic diseasesDéborah Mathis, Joanne Croft, Petr Chrastina, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|December 8, 2016
A simple dried blood spot-method for in vivo measurement of ureagenesis by gas chromatography-mass spectrometry using stable isotopesGabriella Allegri, Sereina Deplazes, Hiu Man Grisch-Chan, et al.
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Showing results (1-10 of 26) with videos related to

Sort By:
Pageof 3
Molecular Genetics and Metabolism Reports|December 13, 2021
Diagnosis of atypical myopathy based on organic acid and acylcarnitine profiles and evolution of biomarkers in surviving horsesDéborah Mathis, Jörn Oliver Sass, Claudia Graubner, et al.
Journal of Inherited Metabolic Disease|February 16, 2019
New insights into human lysine degradation pathways with relevance to pyridoxine-dependent epilepsy due to antiquitin deficiencyLisa M Crowther, Déborah Mathis, Martin Poms, et al.
Journal of Inherited Metabolic Disease|April 23, 2020
LC-MS/MS method for the differential diagnosis of treatable early onset inherited metabolic epilepsiesDéborah Mathis, Karin Beese, Carmen Rüegg, et al.
Journal of Inherited Metabolic Disease|September 5, 2024
Intra- and extracellular real-time analysis of perfused fibroblasts using an NMR bioreactor: A pilot studyChristian Urzì, Christoph Meyer, Déborah Mathis, et al.
Diabetologia|July 8, 2025
Dapagliflozin's impact on hormonal regulation and ketogenesis in type 1 diabetes: a randomised controlled crossover trialAndreas Gübeli, Nicole Steiner, Andreas Limacher, et al.
Genes|October 27, 2022
<i>ACADM</i> Frameshift Variant in Cavalier King Charles Spaniels with Medium-Chain Acyl-CoA Dehydrogenase DeficiencyMatthias Christen, Jos Bongers, Déborah Mathis, et al.
JIMD Reports|March 17, 2021
Decrease of disease-related metabolites upon fasting in a hemizygous knock-in mouse model (<i>Mut</i>-ko/ki) of methylmalonic aciduriaMarie Lucienne, Déborah Mathis, Nathan Perkins, et al.
Journal of the American Chemical Society|May 30, 2008
Artificial metalloenzyme for enantioselective sulfoxidation based on vanadyl-loaded streptavidinAnca Pordea, Marc Creus, Jaroslaw Panek, et al.
Journal of Inherited Metabolic Disease|May 13, 2022
The role of ERNDIM diagnostic proficiency schemes in improving the quality of diagnostic testing for inherited metabolic diseasesDéborah Mathis, Joanne Croft, Petr Chrastina, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|December 8, 2016
A simple dried blood spot-method for in vivo measurement of ureagenesis by gas chromatography-mass spectrometry using stable isotopesGabriella Allegri, Sereina Deplazes, Hiu Man Grisch-Chan, et al.
Pageof 3